1.
Bol Asoc Med P R
; 105(4): 52-5, 2013.
Artigo
em Inglês
| MEDLINE
| ID: mdl-25154176
RESUMO
Adrenocortical carcinoma (ACC) is a rare neoplasm in children. Most patients with ACC suffer syndromes of adrenal hormone overproduction including hypercortisolism, hyperaidosteronism or virilization. We describe the case of an infant girl who presented features of virilization associated with elevated testosterone and DHEA levels due to the presence of a left adrenal cortical carcinoma. A dramatic regression of virilization features occurred after adrenalectomy.