RESUMO

An eight-year-old girl developed optic neuritis followed by primary Sjögren's syndrome confirmed by a lip biopsy. Glucocorticoid therapy combined during six months with monthly intravenous pulse cyclophosphamide ensured resolution of the sicca syndrome but failed to improve the visual impairment. This is the second pediatric case of optic neuritis associated with primary Sjögren's syndrome, and the first pediatric case in which optic neuritis was the only neurologic manifestation.

Assuntos

Hipertensão Intracraniana/complicações , Neurite Óptica/etiologia , Síndrome de Sjogren/complicações , Adolescente , Biópsia por Agulha , Criança , Diagnóstico Diferencial , Feminino , Seguimentos , Glucocorticoides/uso terapêutico , Humanos , Hipertensão Intracraniana/diagnóstico , Hipertensão Intracraniana/patologia , Neurite Óptica/diagnóstico , Neurite Óptica/tratamento farmacológico , Prednisolona/uso terapêutico , Síndrome de Sjogren/diagnóstico