RESUMO

We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now from crisis of angiocholitis.

Assuntos

Doença de Caroli , Doença de Caroli/complicações , Doença de Caroli/diagnóstico , Doença de Caroli/terapia , Feminino , Humanos , Pessoa de Meia-Idade