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Síndrome de Brown bilateral / Bilateral Brown syndrome
Gamio, Susana; Prieto-Díaz, Julio.
Afiliação
  • Gamio, Susana; Hospital de Niños Ricardo Gutiérrez. AR
  • Prieto-Díaz, Julio; Instituto Prieto-Díaz. La Plata. AR
Arch. chil. oftalmol ; 63(2): 335-342, nov. 2005.
Article em Es | LILACS | ID: lil-729259
Biblioteca responsável: CL1.1
RESUMEN

Objetivo:

El síndrome de Brown (SB) se caracteriza por restricción activa y pasiva de la elevación en adducción. Puede ser congénito o adquirido, intermitente o permanente, uni o bilateral; este último se presenta en el 10 por ciento de los casos. Nuestro objetivo es describir 9 casos de SB bilateral y revisar la literatura al respecto. Pacientes se describen características clínicas de 9 casos y se revisa la literatura.

Resultados:

De los 9 casos, 2 eran de sexo masculino, y 7 de sexo femenino. Edad promedio 5.7 años. 1 caso intermitente. Los casos publicados en diferentes series son 13/126 (Brown), 3/8 (Clark y Noel), 7/36 (Waddell ) y 1/30 (Eustis). Entre los casos bilaterales hay alta incidencia de casos familiares.

Conclusión:

Se confirma que el cuadro es más común en mujeres. 7/9 tenía alineamiento en posición primaria. Todos tenían déficit bilateral de elevación y anisotropía en V. Frente a un caso de SB bilateral es conveniente examinar a los familiares en busca de casos asintomáticos.
ABSTRACT

Objective:

The motility defect known as Brown´s síndrome is characterized by active and passive restriction of elevation in adduction. It may be either congenital or acquired, intermittent or permanent, uni or bilateral. It is bilateral in 10 percent of cases. Our purpose is to report 9 cases with bilateral Brown´s syndrome and review the cases previously published. Patients 9 cases are described 2 males and 7 females, average age 5,7 years who had bilateral Brown´s syndrome and review.

Results:

9 cases are described 2 males and 7 females, average age 5,7 years who had bilateral Brown´s syndrome, 1 of them was intermittent. Bilateral cases published are 13/126 in Brown´s series, 3/28 in Clark and Noel´s, 7/36 in Waddell´s and 1/30 in that of Eustis. Among bilateral cases there is a striking incidence of familial cases.

Conclusion:

Brown´s statement that the disorder is more common in females than in males is confirmed in our series. It should be noted that 7 out of 9 of these patients had normal alignment in primary gaze. All cases had bilateral elevation deficit and V pattern. In bilateral cases examination of the relatives should be performed in order to detect asymptomatic familial cases.
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Coleções: 01-internacional Base de dados: LILACS Assunto principal: Transtornos da Motilidade Ocular / Movimentos Oculares Limite: Child / Child, preschool Idioma: Es Revista: Arch. chil. oftalmol Assunto da revista: OFTALMOLOGIA Ano de publicação: 2005 Tipo de documento: Article / Congress and conference País de afiliação: Argentina País de publicação: Chile
Buscar no Google
Coleções: 01-internacional Base de dados: LILACS Assunto principal: Transtornos da Motilidade Ocular / Movimentos Oculares Limite: Child / Child, preschool Idioma: Es Revista: Arch. chil. oftalmol Assunto da revista: OFTALMOLOGIA Ano de publicação: 2005 Tipo de documento: Article / Congress and conference País de afiliação: Argentina País de publicação: Chile